February 11, 2019


Key words: Chagas disease. Fecaloma. Megacolon. Surgical treatment. Palabras clave: Enfermedad de Chagas. Megacolon. Fecaloma. Tratamiento quirúrgico. Diagnóstico y tratamiento de la enfermedad inflamatoria intestinal: Primer . bolsa, anastomosis íleo-anal, pouchitis, complicaciones, megacolon tóxico y. JARAMILLO BARBERI, Lina Eugenia. Proposed Recommendations and Guidelines for Diagnosis of Hirschsprung’s Disease in Mucosal and Submucosal .

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Some patients reach adulthood without a diagnosis for this disease. In this latter case, HD may affect the entire colon and even the small intestine. Chagas disease CHD is endemic in the Americas but due to increased immigration is becoming increasingly common in our country.

Enfermedad de Hirschsprung

The girl was discharged on the 5th day after surgery. Recurrrrence of chagasic megacolon after surgical treatment: Female patient, 13 years old, coming from Campo Grande – MS, reports that since birth had intestinal constipation, with mean bowel movements at every days with hardened feces, being followed-up by a hirscheprung and in treatment for functional constipation.

Therefore, fecal incontinence can cause ds disturbances to patients, with subsequent relationship problems at school and with their own families. Complaints of fecal incontinence are often reported in the literature in cases of functional constipation and of idiopathic megacolon. HD occurs in approximately 1 in live births. Dear EditorChagas disease CHD is endemic in the Americas but due to increased nefermedad is becoming increasingly common in our country.

Chagas disease in the differential diagnosis of megacolon. J Pediatr Rio de J. This clinical course is atypical; in the literature review, only three similar cases were related in association with Hirschsprung disease. Long term follow-up of abdominal rectosigmoidectomy diagnostivo posterior end-to-side stapled anastomosis for chagas megacolon.

This factor contributed to the delay in her diagnosis, driving the pediatrician out of a HD hypothesis.


The absence of ganglion cells results in permanent contraction of the affected segment, preventing the passage of fecal content through that region. Several procedures are used to manage this disease after childhood; currently the option of choice is the surgical procedure of Duhamel.

Rectosigmoidectomy with Ileal Loop Interposition. The diagnosis of HD is supported by barium enema studies, anorectal manometry and rectal biopsy. Nevertheless, the literature considers as the procedure of choice the Duhamel technique in only one surgical time, 2 which reduces the hospitalization time.

Enfermedad de Hirschsprung | West Palm Medical Group

Enterocolitis, constipation and fecal incontinence represent the main postoperative complications in children. The infrequency of this diagnosis in this age and the clinical course of this patient underscore the uniqueness of this case. The technique considered as the golden standard for the diagnosis of HD is the absence of ganglion cells in a rectal biopsy specimen.

World J Surg 15 Enfermedad de Hirschsprung en adultos. Gynecological pathology was ruled out and was done Rx abdomen showing abundant fecal material.

Enfermedad de Hirschsprung en el adulto. Hirschsprung’s Disease HDalso known as congenital aganglionic megacolon, is an anomaly characterized by an absence of enfermrdad cells in the myenteric and submucosal plexuses in a variable bowel segment.

Hirschsprung disease and hypoganglionosis in adults: Conservative treatment is reserved for patients oligosymptomatic or with surgical contraindications 5. Subsequently, new variations have been postulated as the rectosigmoidectomy with ileal interposition, with enfermedav results and decreased recurrence 9, Principles and practice of surgery hirschsprjng the colon, rectum and anus.

The other is the Habr-Gama technique that causes the posterior colorectal anastomosis, immediately, with acceptable results 8.

Serology for Chagas’ disease was carried out in order to exclude a diagnosis of Chagas’ Disease megacolon, with negative result. This surgery is considered curative. In addition, it is established that factors related to gender play a role, since men are preferentially affected, at a frequency of 4: Informe de um caso.


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CHD serology was performed being positive. For our patient, fecal incontinence is a more limiting symptom than the constipation itself, because the girl was living in constant fear of occurrence of such fact in environments like her school, which would cause great encermedad before other people. Some cases involve gene mutations for endothelin-B receptor.

Currently the two most accepted are the Duhamel-Haddad technique 6,7which takes place two times and has the disadvantage of carrying a temporary perineal colostomy. HD presents itself by symptoms of constipation, such as a greater than h delay in elimination of meconium, abdominal distention and vomiting.

Enfermedad de Hirschsprung (para Padres)

The CHD has three phases: The girl refers onset of fecal incontinence at the age of On examination, she presented lower abdominal discomfort with feeling lower abdominal mass. Critical analysis of outcome enfermsdad operative methods. Acta Cir Bras ;23 suppl,1: Typically, patients go to the doctor with a long-standing history of constipation requiring frequent laxative use. Hirschsprun Colon Rectum ;46 11 The objective of this study is to report a case of late diagnosis of the disease at age 13, with symptoms of fecal incontinence in its evolution.

During admission the patient was interrogated again and in her family history stands out the death of his mother for cardiac disease at the age of The diagnosis depends on the stage of the disease and treatment is applicable only in the acute phase.